Which enzyme is deficient in the genetic disorder known as Pompe disease?

A Alpha-galactosidase
B Alpha-glucosidase ✓
C Beta-glucosidase
D Beta-galactosidase

Explanation

Pompe disease is a genetic disorder caused by a deficiency of the enzyme alpha-glucosidase, which is necessary for breaking down glycogen.

Source

OMIM database
Enzymes in Disease Genetics Lysosomal Storage Diseases Hard MEDICAL Confidence: high